Session Title: Quick Fire Free Paper 2
Session Date/Time: Thursday 11/09/2014 | 11:00-12:30
Paper Time: 11:20
Venue: Boulevard D
First Author: : E.Merce FRANCE
Co Author(s): : M. Fortane
To report a case of a fourth-ventricular ependymoma with bilateral chorioretinal folds as its initial presentation.
Chorioretinal folds are an unusual presentation of an intracranial ependymoma. Ependymomas are rare and slow-growing tumors of the central nervous system. They may present with symptoms related to cerebrospinal fluid obstruction or mass effect.
A 49-year-old female patient complained of progressive blurring of both eyes with headache. Fundus examination revealed bilateral chorioretinal folds. Autofluorescence imaging noninvasively demonstrates the pathognomonic pattern of alternating light and dark bands.
Computed tomography and magnetic resonance imaging revealed a mass in the fourth ventricle causing obstructive hydrocephalus. An initial insertion of a ventriculo-peritoneal shunt to deal with the acute intracranial hypertension was done. Subsequently, craniectomy and sub-total resection of the tumour were performed successfully. Histological examination showed an anaplastic ependymoma (WHO grade II-III).
Certain underling diseases associated with chorioretinal folds are lethal and require prompt management. Ophthalmologists should evaluate these patients carefully.